Carnitine palmitoyltransferase 2

AltitudeomicsDB
Protein Official symbol CPT2
Aliases CPT2 CPT1
Chromosomal Location 1
Length 658
Uniprot ID P23786
EC number 2.3.1.21
Protein family Information(Pfam) PF00755;
PDB id None
InterPro ID IPR000542;IPR039551;IPR042232;IPR042231;
dbSNP rs28936375 rs74315294 rs515726177 rs28936674 rs74315300 rs515726174 rs74315298 rs764849762 rs2229291 rs1799821 rs74315295 rs74315297 rs749895856 rs74315296 rs368311455 rs186044004 rs28936376 rs1871748 rs751557097 rs28936673 rs74315293 rs1799822

Protein Protein Interaction

0%
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AltitudeomicsDB
Protein 1 Protein 2 Combine Score
NCOA1 CREBBP 0.999
RXRA NCOA1 0.997
RXRA NCOA2 0.997
PPARA NCOA1 0.993
RXRA CREBBP 0.991
RXRA MED1 0.989
PPARA FABP1 0.988
NCOA2 CREBBP 0.987
TBL1XR1 SMARCD3 0.986
CARM1 CREBBP 0.984
NCOA2 CARM1 0.984
ACOX1 CPT1A 0.982
SMARCD3 TBL1X 0.982
PPARA ACADM 0.979
ACADVL CPT2 0.978
PPARA ACOX1 0.977
CPT2 ACADM 0.977
NCOA6 TGS1 0.977
NCOA1 CARM1 0.976
CPT2 ACOX1 0.976
PPARA CPT1A 0.974
CPT2 ACADL 0.972
NCOA6 MED1 0.97
HELZ2 TGS1 0.969
MED1 TGS1 0.969
NCOA1 NCOA6 0.968
PPARA MED1 0.966
NCOA6 CREBBP 0.966
NCOA1 MED1 0.966
HELZ2 PPARA 0.965
PPARA CREBBP 0.964
CPT2 ACOX3 0.964
HELZ2 CARM1 0.964
NCOA2 MED1 0.963
CRAT ACOX1 0.962
FABP1 ACOX1 0.962
PPARA CPT2 0.962
NCOA2 PPARA 0.961
CPT2 CRAT 0.961
NCOA2 NCOA1 0.958
RXRA PPARA 0.958
FABP1 CPT1A 0.958
NCOA2 NCOA6 0.957
ACADM ACOX1 0.956
RXRA NCOA6 0.953
CHD9 HELZ2 0.952
CPT2 FABP1 0.952
HELZ2 NCOA6 0.952
CARM1 MED1 0.951
MED1 CREBBP 0.951
SLC25A20 CRAT 0.946
CARM1 TGS1 0.946
CHD9 TGS1 0.945
HELZ2 NCOA1 0.945
RXRA SMARCD3 0.944
NCOA6 CARM1 0.943
ACADM FABP1 0.943
CPT2 SLC25A20 0.943
HELZ2 MED1 0.942
TBL1XR1 CREBBP 0.942
CHD9 SMARCD3 0.941
HELZ2 CREBBP 0.94
CREBBP TGS1 0.938
TBL1XR1 TBL1X 0.936
CHD9 RXRA 0.936
CHD9 PPARA 0.936
CPT2 CPT1A 0.934
CPT1B CPT2 0.934
CPT1C CPT2 0.933
RXRA CPT1A 0.933
CHD9 CREBBP 0.932
CREBBP SMARCD3 0.932
ACOX3 CRAT 0.932
RXRA ACOX1 0.931
ACOX3 ACOX1 0.929
CREBBP TBL1X 0.928
CHD9 NCOA6 0.927
CHD9 MED1 0.927
ACADVL ACOX1 0.927
CARM1 SMARCD3 0.926
ACOX1 ACADL 0.926
RXRA FABP1 0.926
RXRA ACADM 0.925
NCOA1 SMARCD3 0.924
RXRA CARM1 0.924
PPARA NCOA6 0.922
NCOA2 SMARCD3 0.922
CPT1B CRAT 0.922
CHD9 NCOA1 0.921
CHD9 CARM1 0.921
RXRA TBL1X 0.921
CRAT CPT1A 0.919
CPT1C CRAT 0.919
HELZ2 SMARCD3 0.918
RXRA HELZ2 0.918
NCOA6 SMARCD3 0.916
ACADM ACADL 0.915
MED1 SMARCD3 0.915
PPARA SMARCD3 0.915
MED1 ACOX1 0.913
NCOA1 TGS1 0.913
TBL1XR1 NCOA6 0.912
NCOA1 FABP1 0.912
NCOA1 TBL1X 0.912
CHD9 NCOA2 0.912
RXRA CPT2 0.911
TBL1XR1 NCOA2 0.91
NCOA6 TBL1X 0.91
FABP1 CREBBP 0.91
CHD9 TBL1XR1 0.909
CPT1A CREBBP 0.909
CPT1B SLC25A20 0.908
CHD9 TBL1X 0.908
NCOA2 TGS1 0.908
CARM1 TBL1X 0.908
ACADM SMARCD3 0.908
MED1 FABP1 0.908
NCOA1 CPT1A 0.908
MED1 TBL1X 0.908
MED1 CPT1A 0.907
TBL1XR1 MED1 0.907
PPARA CARM1 0.907
NCOA2 TBL1X 0.907
CPT1A SMARCD3 0.907
RXRA TBL1XR1 0.907
TBL1XR1 CARM1 0.906
NCOA1 ACOX1 0.906
PPARA TGS1 0.906
NCOA1 ACADM 0.905
CHD9 CPT2 0.905
CPT2 SMARCD3 0.905
HELZ2 NCOA2 0.904
ACOX1 CREBBP 0.904
HELZ2 CPT1A 0.904
TBL1XR1 ACADM 0.904
NCOA2 CPT1A 0.903
HELZ2 TBL1XR1 0.903
TBL1XR1 NCOA1 0.903
HELZ2 TBL1X 0.903
CARM1 CPT1A 0.903
CPT2 CREBBP 0.902
TBL1XR1 TGS1 0.902
HELZ2 ACADM 0.902
SMARCD3 TGS1 0.902
NCOA2 ACADM 0.902
HELZ2 FABP1 0.902
NCOA2 FABP1 0.902
ACADM CARM1 0.902
TGS1 TBL1X 0.902
ACADM CREBBP 0.901
NCOA6 CPT1A 0.901
FABP1 SMARCD3 0.901
FABP1 TBL1X 0.901
ACADM MED1 0.901
CPT2 TBL1X 0.901
FABP1 TGS1 0.9
NCOA6 FABP1 0.9
CPT1A TBL1X 0.9
TBL1XR1 FABP1 0.9
CHD9 CPT1A 0.9
TBL1XR1 CPT1A 0.9
HELZ2 CPT2 0.9
NCOA6 CPT2 0.9
PPARA TBL1X 0.9
ACADM TBL1X 0.9
NCOA2 CPT2 0.9
CPT2 CARM1 0.9
RXRA TGS1 0.9
CPT2 TGS1 0.9
CHD9 FABP1 0.9
CHD9 ACADM 0.9
CPT2 MED1 0.9
ACADM TGS1 0.9
TBL1XR1 PPARA 0.9
CARM1 FABP1 0.9
CPT1A TGS1 0.9
NCOA1 CPT2 0.9
NCOA6 ACADM 0.9
TBL1XR1 CPT2 0.9
Gene Ontology Semantic Similarity
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# 1387 (CREBBP) 8648 (NCOA1) 10499 (NCOA2) 5469 (MED1) 2168 (FABP1) 6604 (SMARCD3) 10498 (CARM1) 1374 (CPT1A) 6907 (TBL1X) 34 (ACADM) 1376 (CPT2) 51 (ACOX1) 96764 (TGS1) 33 (ACADL) 23054 (NCOA6) 5465 (PPARA) 8310 (ACOX3) 1384 (CRAT) 85441 (HELZ2) 788 (SLC25A20) 6256 (RXRA) 79718 (TBL1XR1) 37 (ACADVL) 1375 (CPT1B) 126129 (CPT1C)
1387 (CREBBP) 1.00 0.64 0.64 0.70 0.47 0.56 0.55 0.48 0.65 0.37 0.48 0.40 0.47 0.19 0.62 0.71 0.36 0.46 0.54 0.12 0.67 0.60 0.20 0.51 0.51
8648 (NCOA1) 0.64 1.00 0.95 0.81 0.58 0.80 0.57 0.11 0.70 0.43 0.11 0.54 0.53 0.16 0.84 0.64 0.48 0.54 0.67 0.12 0.67 0.70 0.20 0.55 0.55
10499 (NCOA2) 0.64 0.95 1.00 0.80 0.58 0.81 0.57 0.11 0.74 0.42 0.11 0.52 0.51 0.16 0.80 0.63 0.45 0.52 0.69 0.12 0.67 0.69 0.20 0.54 0.54
5469 (MED1) 0.70 0.81 0.80 1.00 0.49 0.71 0.60 0.11 0.71 0.37 0.11 0.46 0.45 0.16 0.79 0.75 0.43 0.45 0.61 0.12 0.78 0.66 0.19 0.47 0.47
2168 (FABP1) 0.47 0.58 0.58 0.49 1.00 0.59 0.39 0.14 0.69 0.47 0.14 0.48 0.55 0.22 0.56 0.40 0.40 0.51 0.50 0.15 0.44 0.66 0.25 0.62 0.62
6604 (SMARCD3) 0.56 0.80 0.81 0.71 0.59 1.00 0.49 0.08 0.71 0.41 0.08 0.49 0.50 0.15 0.79 0.42 0.47 0.60 0.64 0.09 0.47 0.67 0.19 0.55 0.55
10498 (CARM1) 0.55 0.57 0.57 0.60 0.39 0.49 1.00 0.22 0.64 0.32 0.22 0.35 0.58 0.19 0.56 0.49 0.31 0.32 0.52 0.12 0.57 0.62 0.20 0.38 0.38
1374 (CPT1A) 0.48 0.11 0.11 0.11 0.14 0.08 0.22 1.00 0.11 0.16 1.00 0.13 0.22 0.16 0.11 0.11 0.13 0.56 0.11 0.04 0.11 0.11 0.16 1.00 1.00
6907 (TBL1X) 0.65 0.70 0.74 0.71 0.69 0.71 0.64 0.11 1.00 0.51 0.11 0.54 0.62 0.19 0.71 0.58 0.48 0.54 0.70 0.12 0.68 0.95 0.23 0.66 0.66
34 (ACADM) 0.37 0.43 0.42 0.37 0.47 0.41 0.32 0.16 0.51 1.00 0.16 0.52 0.42 0.66 0.41 0.30 0.50 0.35 0.36 0.09 0.34 0.48 0.71 0.43 0.43
1376 (CPT2) 0.48 0.11 0.11 0.11 0.14 0.08 0.22 1.00 0.11 0.16 1.00 0.13 0.22 0.16 0.11 0.11 0.13 0.56 0.11 0.04 0.11 0.11 0.16 1.00 1.00
51 (ACOX1) 0.40 0.54 0.52 0.46 0.48 0.49 0.35 0.13 0.54 0.52 0.13 1.00 0.44 0.63 0.47 0.39 0.91 0.45 0.42 0.09 0.44 0.53 0.45 0.46 0.46
96764 (TGS1) 0.47 0.53 0.51 0.45 0.55 0.50 0.58 0.22 0.62 0.42 0.22 0.44 1.00 0.22 0.49 0.36 0.36 0.45 0.42 0.12 0.41 0.58 0.24 0.53 0.53
33 (ACADL) 0.19 0.16 0.16 0.16 0.22 0.15 0.19 0.16 0.19 0.66 0.16 0.63 0.22 1.00 0.16 0.19 0.69 0.16 0.20 0.07 0.21 0.19 0.82 0.18 0.18
23054 (NCOA6) 0.62 0.84 0.80 0.79 0.56 0.79 0.56 0.11 0.71 0.41 0.11 0.47 0.49 0.16 1.00 0.49 0.43 0.48 0.67 0.12 0.56 0.68 0.20 0.52 0.52
5465 (PPARA) 0.71 0.64 0.63 0.75 0.40 0.42 0.49 0.11 0.58 0.30 0.11 0.39 0.36 0.19 0.49 1.00 0.36 0.30 0.49 0.12 0.80 0.54 0.19 0.37 0.37
8310 (ACOX3) 0.36 0.48 0.45 0.43 0.40 0.47 0.31 0.13 0.48 0.50 0.13 0.91 0.36 0.69 0.43 0.36 1.00 0.40 0.35 0.09 0.40 0.44 0.50 0.37 0.37
1384 (CRAT) 0.46 0.54 0.52 0.45 0.51 0.60 0.32 0.56 0.54 0.35 0.56 0.45 0.45 0.16 0.48 0.30 0.40 1.00 0.37 0.09 0.37 0.51 0.18 0.69 0.69
85441 (HELZ2) 0.54 0.67 0.69 0.61 0.50 0.64 0.52 0.11 0.70 0.36 0.11 0.42 0.42 0.20 0.67 0.49 0.35 0.37 1.00 0.12 0.56 0.68 0.19 0.45 0.45
788 (SLC25A20) 0.12 0.12 0.12 0.12 0.15 0.09 0.12 0.04 0.12 0.09 0.04 0.09 0.12 0.07 0.12 0.12 0.09 0.09 0.12 1.00 0.12 0.12 0.07 0.12 0.12
6256 (RXRA) 0.67 0.67 0.67 0.78 0.44 0.47 0.57 0.11 0.68 0.34 0.11 0.44 0.41 0.21 0.56 0.80 0.40 0.37 0.56 0.12 1.00 0.65 0.20 0.42 0.42
79718 (TBL1XR1) 0.60 0.70 0.69 0.66 0.66 0.67 0.62 0.11 0.95 0.48 0.11 0.53 0.58 0.19 0.68 0.54 0.44 0.51 0.68 0.12 0.65 1.00 0.22 0.63 0.63
37 (ACADVL) 0.20 0.20 0.20 0.19 0.25 0.19 0.20 0.16 0.23 0.71 0.16 0.45 0.24 0.82 0.20 0.19 0.50 0.18 0.19 0.07 0.20 0.22 1.00 0.21 0.21
1375 (CPT1B) 0.51 0.55 0.54 0.47 0.62 0.55 0.38 1.00 0.66 0.43 1.00 0.46 0.53 0.18 0.52 0.37 0.37 0.69 0.45 0.12 0.42 0.63 0.21 1.00 1.00
126129 (CPT1C) 0.51 0.55 0.54 0.47 0.62 0.55 0.38 1.00 0.66 0.43 1.00 0.46 0.53 0.18 0.52 0.37 0.37 0.69 0.45 0.12 0.42 0.63 0.21 1.00 1.00
Association with High Altitude
Protein Official symbol Source Organism Tissue of Expression Level of hypoxia Altitude Duration of experiment Level of expression Fold change Experiment details geographical location ethnicity of the patients Control group Control (Fold change) Reference (PMID)
CPT2 Human Blood - 3250 m 4 day upregulated 4.8121 Microarray Himalayas Indians 1 Sea level healthy individuals 24465776
Association with TF
TF TF Entrez Gene Gene Entrez Type PMID Database
Association with miRNA
miRTarBase ID miRNA Species (miRNA) Protein Official Symbol Human Entrez ID Species (Target Gene) Experiments Support Type References (PMID)
MIRT025385 hsa-miR-34a-5p Homo sapiens CPT2 1376 Homo sapiens Proteomics Functional MTI (Weak) 21566225
MIRT043910 hsa-miR-378a-3p Homo sapiens CPT2 1376 Homo sapiens CLASH Functional MTI (Weak) 23622248
Gene Ontology
ID GO ID GO Term GO Type
1376 GO:0005654 nucleoplasm GOTERM_CC_DIRECT
1376 GO:0005743 mitochondrial inner membrane GOTERM_CC_DIRECT
1376 GO:0005730 nucleolus GOTERM_CC_DIRECT
1376 GO:0006635 fatty acid beta-oxidation GOTERM_BP_DIRECT
1376 GO:0004095 carbonate dehydratase activity GOTERM_MF_DIRECT
1376 GO:0006853 carnitine shuttle GOTERM_BP_DIRECT
1376 GO:0016746 transferase activity GOTERM_MF_DIRECT
1376 GO:0005739 mitochondrion GOTERM_CC_DIRECT
Pathways
Human Entrez ID KEGG ID KEGG Term
1376 hsa00071 Fatty acid degradation
1376 hsa03320 PPAR signaling pathway
1376 hsa01212 Fatty acid metabolism
Association with Disease
Protein Official Symbol Human Entrez ID Disease Name Disease Id Disease Semantic Type Semantic score DSI DPI Disease Type
CPT2 1376 Central Nervous System Metabolic Disorders C0750968 Disease or Syndrome 0.3 0.596 0.483 disease
CPT2 1376 Acquired Metabolic Diseases, Nervous System C1135773 Disease or Syndrome 0.3 0.596 0.483 phenotype
CPT2 1376 Brain Diseases, Metabolic C0006112 Disease or Syndrome 0.3 0.596 0.483 group
CPT2 1376 Myopathy C0026848 Disease or Syndrome 0.43 0.596 0.483 group
CPT2 1376 Brain Diseases, Metabolic, Acquired C0751744 Disease or Syndrome 0.3 0.596 0.483 disease
CPT2 1376 Metabolic Disorder, Central Nervous System, Acquired C0751743 Disease or Syndrome 0.3 0.596 0.483 disease
CPT2 1376 ENCEPHALOPATHY, ACUTE, INFECTION-INDUCED, SUSCEPTIBILITY TO, 4 C3280160 Finding 0.4 0.596 0.483 phenotype
CPT2 1376 CARNITINE PALMITOYLTRANSFERASE II DEFICIENCY, LETHAL NEONATAL C1833518 Disease or Syndrome 0.6 0.596 0.483 disease
CPT2 1376 CARNITINE PALMITOYLTRANSFERASE II DEFICIENCY, LATE-ONSET C1833508 Disease or Syndrome 0.7 0.596 0.483 disease
CPT2 1376 CARNITINE PALMITOYLTRANSFERASE II DEFICIENCY, INFANTILE C1833511 Disease or Syndrome 0.71 0.596 0.483 disease
CPT2 1376 Rhabdomyolysis C0035410 Pathologic Function 0.42 0.596 0.483 phenotype
CPT2 1376 Hyperammonemia C0220994 Disease or Syndrome 0.4 0.596 0.483 phenotype
CPT2 1376 Arthrogryposis C0003886 Disease or Syndrome 0.3 0.596 0.483 disease
CPT2 1376 Congenital myopathy (disorder) C0270960 Congenital Abnormality 0.3 0.596 0.483 group
Association with Drug
Protein Official Symbol Human Entrez ID drug_claim_primary_name drug_name drug_chembl_id interaction_types
CPT2 1376 (S)-ARN2508 None None inhibitor
CPT2 1376 (R)-ARN2508 None None inhibitor
CPT2 1376 ASPIRIN ASPIRIN CHEMBL25 inhibitor
CPT2 1376 BENZQUINAMIDE BENZQUINAMIDE CHEMBL1201250 inhibitor
CPT2 1376 CARPROFEN CARPROFEN CHEMBL1316 inhibitor
CPT2 1376 CELECOXIB CELECOXIB CHEMBL118 inhibitor
CPT2 1376 DICLOFENAC DICLOFENAC CHEMBL139 inhibitor
CPT2 1376 ESFLURBIPROFEN ESFLURBIPROFEN CHEMBL435298 inhibitor
CPT2 1376 ETORICOXIB ETORICOXIB CHEMBL416146 inhibitor
CPT2 1376 ETODOLAC ETODOLAC CHEMBL622 inhibitor
CPT2 1376 FLURBIPROFEN FLURBIPROFEN CHEMBL563 inhibitor
CPT2 1376 IBUPROFEN IBUPROFEN CHEMBL521 inhibitor
CPT2 1376 KETOROLAC KETOROLAC CHEMBL469 inhibitor
CPT2 1376 KETOPROFEN KETOPROFEN CHEMBL571 inhibitor
CPT2 1376 LUMIRACOXIB LUMIRACOXIB CHEMBL404108 inhibitor
CPT2 1376 MECLOFENAMIC ACID MECLOFENAMIC ACID CHEMBL509 inhibitor
CPT2 1376 MEFENAMIC ACID MEFENAMIC ACID CHEMBL686 inhibitor
CPT2 1376 MELOXICAM MELOXICAM CHEMBL599 inhibitor
CPT2 1376 NAPROXCINOD NAPROXCINOD CHEMBL2103831 inhibitor
CPT2 1376 NAPROXEN NAPROXEN CHEMBL154 inhibitor
CPT2 1376 NIMESULIDE NIMESULIDE CHEMBL56367 inhibitor
CPT2 1376 NS-398 NS-398 CHEMBL7162 inhibitor
CPT2 1376 OXAPROZIN OXAPROZIN CHEMBL1071 inhibitor
CPT2 1376 PARACETAMOL ACETAMINOPHEN CHEMBL112 inhibitor
CPT2 1376 PERHEXILINE PERHEXILINE CHEMBL75880 None
CPT2 1376 PERHEXILINE PERHEXILINE CHEMBL75880 None
CPT2 1376 PEPTIDE 30 [PMID: 27019010 ] None None inhibitor
CPT2 1376 PHENYLBUTAZONE PHENYLBUTAZONE CHEMBL101 inhibitor
CPT2 1376 PIROXICAM PIROXICAM CHEMBL527 inhibitor
CPT2 1376 PROPIONYL-L-CARNITINE None None None
CPT2 1376 RESVERATROL RESVERATROL CHEMBL165 inhibitor
CPT2 1376 ROFECOXIB ROFECOXIB CHEMBL122 inhibitor
CPT2 1376 SUPROFEN SUPROFEN CHEMBL956 inhibitor
CPT2 1376 VALDECOXIB VALDECOXIB CHEMBL865 inhibitor