Oral-facial-digital syndrome 1
AltitudeomicsDB
Protein Official symbol |
OFD1 |
Aliases |
OFD1 CXorf5 |
Chromosomal Location |
X |
Length |
1012 |
Uniprot ID |
O75665 |
EC number |
None |
Protein family Information(Pfam) |
PF16045; |
PDB id |
None |
InterPro ID |
IPR006594; |
dbSNP |
rs312262812 rs312262814 rs312262827 rs886039860 rs122460150 |
AltitudeomicsDB
Protein 1 |
Protein 2 |
Combine Score |
CEP290 |
TMEM216 |
0.989 |
CEP290 |
MKS1 |
0.987 |
TMEM216 |
MKS1 |
0.986 |
OFD1 |
C2CD3 |
0.985 |
CEP290 |
CEP131 |
0.981 |
CEP290 |
SDCCAG8 |
0.981 |
SDCCAG8 |
OFD1 |
0.979 |
CEP290 |
PCM1 |
0.978 |
CEP290 |
OFD1 |
0.976 |
OFD1 |
CEP135 |
0.975 |
CEP290 |
CEP135 |
0.975 |
CEP131 |
PCM1 |
0.973 |
CEP131 |
OFD1 |
0.973 |
PCM1 |
CEP72 |
0.972 |
MKS1 |
OFD1 |
0.97 |
OFD1 |
CEP72 |
0.97 |
TMEM216 |
OFD1 |
0.97 |
OFD1 |
PCM1 |
0.97 |
OFD1 |
SCLT1 |
0.969 |
C2CD3 |
SCLT1 |
0.968 |
MKS1 |
SDCCAG8 |
0.966 |
CEP131 |
CEP72 |
0.958 |
CEP290 |
SCLT1 |
0.955 |
SDCCAG8 |
PCM1 |
0.952 |
TMEM216 |
C2CD3 |
0.952 |
CEP290 |
CEP72 |
0.95 |
MKS1 |
C2CD3 |
0.949 |
TMEM216 |
SDCCAG8 |
0.948 |
MKS1 |
SCLT1 |
0.948 |
PCM1 |
CEP135 |
0.947 |
SDCCAG8 |
CEP135 |
0.946 |
CEP290 |
C2CD3 |
0.945 |
SCLT1 |
CEP135 |
0.945 |
C2CD3 |
CEP72 |
0.938 |
CEP131 |
CEP135 |
0.935 |
CEP131 |
SDCCAG8 |
0.93 |
MKS1 |
CEP135 |
0.929 |
CEP131 |
C2CD3 |
0.923 |
TMEM216 |
CEP131 |
0.921 |
CEP72 |
CEP135 |
0.92 |
TMEM216 |
SCLT1 |
0.919 |
CEP131 |
MKS1 |
0.915 |
SDCCAG8 |
CEP72 |
0.913 |
SCLT1 |
CEP72 |
0.912 |
C2CD3 |
CEP135 |
0.911 |
TMEM216 |
CEP72 |
0.909 |
PCM1 |
SCLT1 |
0.906 |
CEP131 |
SCLT1 |
0.905 |
MKS1 |
CEP72 |
0.905 |
C2CD3 |
PCM1 |
0.902 |
SDCCAG8 |
SCLT1 |
0.902 |
SDCCAG8 |
C2CD3 |
0.901 |
MKS1 |
PCM1 |
0.901 |
TMEM216 |
CEP135 |
0.9 |
TMEM216 |
PCM1 |
0.9 |
Gene Ontology Semantic Similarity
Download Tab separated file
# |
80184 (CEP290) |
51259 (TMEM216) |
8481 (OFD1) |
10806 (SDCCAG8) |
22994 (CEP131) |
5108 (PCM1) |
54903 (MKS1) |
26005 (C2CD3) |
55722 (CEP72) |
9662 (CEP135) |
80184 (CEP290)
|
1.00
|
1.00
|
0.87
|
1.00
|
0.83
|
1.00
|
1.00
|
1.00
|
1.00
|
0.91
|
51259 (TMEM216)
|
1.00
|
1.00
|
1.00
|
1.00
|
1.00
|
1.00
|
1.00
|
1.00
|
1.00
|
1.00
|
8481 (OFD1)
|
0.87
|
1.00
|
1.00
|
1.00
|
0.77
|
0.87
|
1.00
|
1.00
|
1.00
|
0.81
|
10806 (SDCCAG8)
|
1.00
|
1.00
|
1.00
|
1.00
|
1.00
|
1.00
|
1.00
|
1.00
|
1.00
|
1.00
|
22994 (CEP131)
|
0.83
|
1.00
|
0.77
|
1.00
|
1.00
|
0.83
|
1.00
|
1.00
|
1.00
|
0.80
|
5108 (PCM1)
|
1.00
|
1.00
|
0.87
|
1.00
|
0.83
|
1.00
|
1.00
|
1.00
|
1.00
|
0.91
|
54903 (MKS1)
|
1.00
|
1.00
|
1.00
|
1.00
|
1.00
|
1.00
|
1.00
|
1.00
|
1.00
|
1.00
|
26005 (C2CD3)
|
1.00
|
1.00
|
1.00
|
1.00
|
1.00
|
1.00
|
1.00
|
1.00
|
1.00
|
1.00
|
55722 (CEP72)
|
1.00
|
1.00
|
1.00
|
1.00
|
1.00
|
1.00
|
1.00
|
1.00
|
1.00
|
1.00
|
9662 (CEP135)
|
0.91
|
1.00
|
0.81
|
1.00
|
0.80
|
0.91
|
1.00
|
1.00
|
1.00
|
1.00
|
Association with High Altitude
Protein Official symbol |
Source Organism |
Tissue of Expression |
Level of hypoxia |
Altitude |
Duration of experiment |
Level of expression |
Fold change |
Experiment details |
geographical location |
ethnicity of the patients |
Control group |
Control (Fold change) |
Reference (PMID) |
OFD1 |
Human |
Blood |
- |
3650 m |
48 hours |
downregulated |
0.642 |
Microarray |
Himalayas |
Indians |
1 |
HAPE Pateints Vs Normal |
http://medind.nic.in/iab/t12/i1/iabt12i1p1.pdf |
Association with miRNA
miRTarBase ID |
miRNA |
Species (miRNA) |
Protein Official Symbol |
Human Entrez ID |
Species (Target Gene) |
Experiments |
Support Type |
References (PMID) |
MIRT029155 |
hsa-miR-26b-5p |
Homo sapiens |
OFD1 |
8481 |
Homo sapiens |
Microarray |
Functional MTI (Weak) |
19088304 |
MIRT050901 |
hsa-miR-17-5p |
Homo sapiens |
OFD1 |
8481 |
Homo sapiens |
CLASH |
Functional MTI (Weak) |
23622248 |
Gene Ontology
ID |
GO ID |
GO Term |
GO Type |
8481 |
GO:0043014 |
peptidoglycan binding |
GOTERM_MF_DIRECT |
8481 |
GO:0036064 |
ciliary basal body |
GOTERM_CC_DIRECT |
8481 |
GO:0005814 |
centriole |
GOTERM_CC_DIRECT |
8481 |
GO:0007099 |
centriole replication |
GOTERM_BP_DIRECT |
8481 |
GO:0005634 |
nucleus |
GOTERM_CC_DIRECT |
8481 |
GO:0060271 |
cilium morphogenesis |
GOTERM_BP_DIRECT |
8481 |
GO:0042802 |
identical protein binding |
GOTERM_MF_DIRECT |
8481 |
GO:0005515 |
protein binding |
GOTERM_MF_DIRECT |
8481 |
GO:0016020 |
membrane |
GOTERM_CC_DIRECT |
8481 |
GO:0060287 |
epithelial cilium movement involved in determination of left/right asymmetry |
GOTERM_BP_DIRECT |
8481 |
GO:0043015 |
ATP-dependent protein binding |
GOTERM_MF_DIRECT |
8481 |
GO:0005929 |
cilium |
GOTERM_CC_DIRECT |
8481 |
GO:0015630 |
microtubule cytoskeleton |
GOTERM_CC_DIRECT |
8481 |
GO:0034451 |
centriolar satellite |
GOTERM_CC_DIRECT |
8481 |
GO:0090307 |
mitotic spindle assembly |
GOTERM_BP_DIRECT |
8481 |
GO:0016021 |
integral component of membrane |
GOTERM_CC_DIRECT |
8481 |
GO:0000086 |
G2/M transition of mitotic cell cycle |
GOTERM_BP_DIRECT |
8481 |
GO:0007067 |
mitotic nuclear division |
GOTERM_BP_DIRECT |
8481 |
GO:0005813 |
centrosome |
GOTERM_CC_DIRECT |
8481 |
GO:0005829 |
cytosol |
GOTERM_CC_DIRECT |
Pathways
Human Entrez ID |
KEGG ID |
KEGG Term |
Association with Disease
Protein Official Symbol |
Human Entrez ID |
Disease Name |
Disease Id |
Disease Semantic Type |
Semantic score |
DSI |
DPI |
Disease Type |
OFD1 |
8481 |
Ciliary Motility Disorders |
C0008780 |
Disease or Syndrome |
0.3 |
0.547 |
0.724 |
group |
OFD1 |
8481 |
Oto-Palato-digital syndrome type 1 |
C0265251 |
Disease or Syndrome |
0.3 |
0.547 |
0.724 |
disease |
OFD1 |
8481 |
RP23 gene |
C1419610 |
Disease or Syndrome |
0.4 |
0.547 |
0.724 |
disease |
OFD1 |
8481 |
SIMPSON-GOLABI-BEHMEL SYNDROME, TYPE 2 (disorder) |
C1846175 |
Disease or Syndrome |
0.43 |
0.547 |
0.724 |
disease |
OFD1 |
8481 |
Orofaciodigital syndrome type1 |
C2931426 |
Disease or Syndrome |
0.56 |
0.547 |
0.724 |
disease |
OFD1 |
8481 |
JOUBERT SYNDROME 10 (disorder) |
C2749019 |
Disease or Syndrome |
0.63 |
0.547 |
0.724 |
disease |
OFD1 |
8481 |
Hydrocephalus |
C0020255 |
Disease or Syndrome |
0.41 |
0.547 |
0.724 |
disease |
OFD1 |
8481 |
Intellectual Disability |
C3714756 |
Mental or Behavioral Dysfunction |
0.41 |
0.547 |
0.724 |
group |
OFD1 |
8481 |
Arthrogryposis |
C0003886 |
Disease or Syndrome |
0.3 |
0.547 |
0.724 |
disease |
OFD1 |
8481 |
Congenital ocular coloboma (disorder) |
C0009363 |
Congenital Abnormality |
0.3 |
0.547 |
0.724 |
disease |
OFD1 |
8481 |
Osteogenesis Imperfecta |
C0029434 |
Congenital Abnormality; Disease or Syndrome |
0.31 |
0.547 |
0.724 |
disease |
OFD1 |
8481 |
Cystic Kidney Diseases |
C1691228 |
Disease or Syndrome |
0.31 |
0.547 |
0.724 |
group |
OFD1 |
8481 |
Ciliopathies |
C4277690 |
Congenital Abnormality |
0.34 |
0.547 |
0.724 |
group |
OFD1 |
8481 |
Polydactyly |
C0152427 |
Congenital Abnormality |
0.4 |
0.547 |
0.724 |
disease |
OFD1 |
8481 |
OROFACIODIGITAL SYNDROME VI |
C2745997 |
Disease or Syndrome |
0.3 |
0.547 |
0.724 |
disease |
OFD1 |
8481 |
Retinitis Pigmentosa |
C0035334 |
Disease or Syndrome |
0.4 |
0.547 |
0.724 |
disease |
OFD1 |
8481 |
Polynesian Bronchiectasis |
C4317124 |
Disease or Syndrome |
0.3 |
0.547 |
0.724 |
disease |
OFD1 |
8481 |
Kartagener Syndrome |
C0022521 |
Disease or Syndrome |
0.3 |
0.547 |
0.724 |
disease |
OFD1 |
8481 |
Orofaciodigital Syndrome I |
C1510460 |
Disease or Syndrome |
0.66 |
0.547 |
0.724 |
disease |
Association with Drug
Protein Official Symbol |
Human Entrez ID |
drug_claim_primary_name |
drug_name |
drug_chembl_id |
interaction_types |